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Differential
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abducens nerve paralysis

acral sensory symptoms

Addison's disease

adrenoleukodystrophy

adrenomyeloneuropathy

adult polyglucosan body disease

advances in neurology

adverse drug reaction

alcohol intolerance

alkylating agents

altered states of consciousness

alternating rapid movement

amyloid angiopathy, cerebral

amyloidosis, oculoleptomeningeal, familial

amyotrophic lateral sclerosis

amyotrophic lateral sclerosis, epidemiology of

amyotrophic lateral sclerosis, familial

amyotrophic lateral sclerosis, guamian type of

ankle reflex, absent

anterior interosseous neuropathy

anterior tibial muscle weakness

arrhythmia, cardiac

arthrogryposis multiplex

arthropathy, neuropathic

arylsulfatase B

ataxia, cerebellar

ataxia, hereditary

ataxia, progressive

ataxia, sensory

ataxia, truncal

auditory evoked brainstem potentials

autonomic dysfunction

autonomic nervous system

autonomic neuropathy

autonomic neuropathy, idiopathic

bacterial infection

Bassen-Kornzweig syndrome

benign essential tremor

bladder dysfunction

blood dyscrasias, neurologic findings with

brachial neuritis

brachial neuritis, acute

brachial neuritis, bilateral

brachial neuritis, prognosis of

brachial plexus

brachial plexus neuropathy

brachial plexus neuropathy, bilateral

brachial plexus neuropathy, familial

brachial plexus neuropathy, recurrent

burning paresthesia

caloric testing

CAT scan, abnormal

CAT scan, metrizamide

CAT scan, myelogram with

cataracts, congenital

cauda equina, enhancement

cauda equina, lesion of

cavernous sinus

cavernous sinus, lesion of

central core disease

cerebellar ataxia, neuropathy and vestibular areflexia syndrome

cerebellar atrophy, secondary

cerebellar lesion

cerebellum, disease of

cerebro hepato renal syndrome

cerebrospinal fluid, pressure low

cerebrospinal fluid, xanthochromia of

cerebrotendinous xanthomatosis

Charcot-Marie-Tooth

chemotherapy, CNS treatment and complications with

cholesterol, HDL

chromosomal abnormality

claudication, intermittent of cauda equina

Clinical Pathologic Conference(C.P.C.)

clubfoot as related to neurologic disease

Cockayne's syndrome

cold temperature

compression neuropathy

compression neuropathy, recurrent

cornea, abnormal

cornea, opacity of

corpus callosum, lesion of

cranial nerve enhancement

cranial nerve enlargement

cranial neuropathy

cranial neuropathy, multiple

degenerative diseases of CNS

Dejerine-Sottas syndrome

demyelinating disease

denervation of muscle

dermatomyositis

diabetes mellitus

differential diagnosis

diplegia, brachial

diplopia, transient

disability, neurological

dissociated sensory loss

distal muscle atrophy

distal muscle weakness

drug induced neurologic disorders

electrocardiogram, abnormal

electroencephalogram, inflammatory disease

electronystagmography

electroretinograph

entrapment neuropathy

enzyme, muscle disease

epidemiology of neurology

episodic neurologic deficits

erythromelalgia

evoked potentials

eye movement, disorders of

face, numbness of

facial nerve palsy, bilateral

facial weakness

facial weakness, bilateral

family planning

Fazio-Londe's disease

fine motor function, impaired

Friedreich's ataxia

fundus, abnormality of

genetic counselling

genetic diagnosis

genetic diagnosis, prenatal

genetic linkage

genetic neurologic disorders

genetic testing

genu of corpus callosum

giant axonal neuropathy

Guillain Barre syndrome

Hallervorden Spatz disease

heavy metal intoxication

heel-knee-shin test

hemiparesis, transient

hepatitis C virus

hepatosplenomegaly

high arched feet

human immunodeficiency virus type 1

hyperthyroidism

idiopathic polyneuropathy

inappropriate antidiuretic(A.D.H.)hormone, CNS involvement with

inclusion bodies

inclusion bodies, eosinophilic cytoplasmic

intellectual deficit

internuclear ophthalmoplegia

intracerebral hemorrhage

intracerebral hemorrhage, familial

intrinsic hand muscles, wasting of

Isaacs syndrome

Kearns-Sayre syndrome

klippel feil syndrome

Korsakoff's psychosis

Kugelberg-Welander syndrome

kyphoscoliosis, neurologic causes of

laminectomy, cervical

laminectomy, lumbar

Laurence-Moon-Bardet-Biedl syndrome

Leber's congenital amaurosis

leg weakness, bilateral

leukemia, neurologic findings assoc.with

leukoencephalopathy

light-near dissociation, causes of

liver transplantation

lumbosacral plexopathy

lumbosacral plexus

lymphadenopathy

macular degeneration

magnetic stimulation

magnetic stimulation, brain

median neuropathy

meningoencephalopathy

mental retardation

methylhydrazine derivatives

midbrain, atrophy

middle cerebellar peduncle, lesion

middle cerebellar peduncle, lesion, bilateral

mitochondrial disease

molecular genetics

monoamine oxidase inhibitors

mononeuropathy multiplex

mononeuropathy, children

mononeuropathy, recurrent

motor neuron disease

movement disorder

MRI, brachial plexus

MRI, contrast enhanced

MRI, cranial nerves

MRI, diffusion tensor

MRI, diffusion weighted

MRI, disappearing lesion on

MRI, peripheral nerve

MRI, spinal cord

mucopolysaccharidoses

muscle atrophy, focal

muscle atrophy, progressive

muscle diseases, characteristics of

muscle hypertrophy

muscle weakness

muscle weakness, proximal

muscle, metabolic disorders of

muscular dystrophy

muscular dystrophy, Duchenne

muscular dystrophy, facioscapulohumeral

muscular dystrophy, limb-girdle

myasthenia gravis

myasthenia gravis, familial incidence of

myasthenia gravis, nystagmus in

myasthenia gravis, ocular

myasthenia gravis, sensory loss with

myasthenic crisis

myelin protein zero gene

myelogram, cervical

myeloneuropathy

myeloradiculopathy

myopathy, carcinomatous

myopathy, mitochondrial

myopathy, thyroid disease causing

myotonia dystrophica

nausea and vomiting

nerve biopsy, indication

nerve conduction studies

nerve conduction studies, sensory

nerve growth factor

nerve growth stimulating activity

nerve hypertrophy

nerve root enhancement

nerve root hypertrophy

neuritis, causes of

neurofibrillary degeneration

neurofibromatosis 1

neurogenic bladder

neurologic complications of, systemic cancer

neurologic complications of, systemic disease

neurologic disease

neurologic disease, diagnoses of

neuromuscular disease, electrodiagnosis of

neuronal ceroid-lipofuscinosis

neuronopathy, sensory

neuropathy, amyloid

neuropathy, ataxic

neuropathy, classification of

neuropathy, demyelinating

neuropathy, diabetic

neuropathy, etiologies of

neuropathy, hereditary peripheral

neuropathy, hypertrophic

neuropathy, motor

neuropathy, onion bulb

neuropathy, peripheral

neuropathy, peripheral, treatment

neuropathy, recurrent

neuropathy, sensory

neuropathy, sensory, hereditary

neuropathy, work up for

next-generation sequencing

night blindness

nitrogen mustard

numbness, extremity

nystagmus, dissociated

nystagmus, gaze-evoked

nystagmus, monocular

optic atrophy, hereditary

optic neuropathy

orthostatic hypotension

orthostatic hypotension, idiopathic

paralysis, recurrent

paraparesis, familial spastic

paraparesis, spastic

paresthesias, feet

paresthesias, lower extremity

patient information and support

peroneal muscle atrophy, causes of

peroneal nerve, lesion of

peroxisomal disease

pheochromocytoma

pigmentary retinopathy

pleocytosis of cerebrospinal fluid

poison, mercury

poison, neurologic problems with

polyglucosan body

polyglucosan body disease

polymerase chain reaction

polyneuropathy, chronic idiopathic

polyneuropathy, chronic inflammatory demyelinating

polyneuropathy, chronic relapsing

polyneuropathy, familial

positional head-hanging test

positive sharp waves

post polio syndrome

precipitating factors

pregnancy, neurologic complications in

progressive neurologic disorder

proximal muscle atrophy

pseudointernuclear ophthalmoplegia

psychological testing

ptosis, bilateral

pulmonary function tests

pupil, abnormality in neurologic disorders

pupil, dilated and fixed, bilateral

pupil, scalloped

pyramidal tract dysfunction

quadriplegia, transient

quality of life

radial nerve, palsy of

reading disorder, acquired

recombinant DNA

recruitment, reduced

refractive errors

Refsum's disease

respiratory failure

retinal degeneration

retinitis pigmentosa

reversible neurologic disorder

Riley-Day syndrome

root lesion, nerve

Roussy Levy syndrome

saccadic eye movements, abnormal

sensorineural hearing loss

sensory ganglia

sensory ganglia, abnormal

sensory loss, truncal

sensory nerve action potentials

sensory polyneuropathy

shoulder, numbness

shoulder, pain in

Shy-Drager syndrome

skin, lesions in neurologic disorders

somatosensory evoked potentials

speech disorder

speech disorder, non aphasic

spinal cord, compression of

spinal muscular atrophy

spinal stenosis

spinal stenosis, familial

spinocerebellar ataxia

spinocerebellar degeneration

splenium of corpus callosum

spontaneous muscle activity

spontaneous remission

steroid therapy, CNS treatment and complications with

stiff man syndrome

strokelike episodes

subdural hematoma

suprascapular neuropathy

symmetric brain lesions

tandem gait, ataxic

Tangier's disease

tapetoretinal degeneration

thalamus, lesion of

thalamus, lesion of-bilateral

thrombocytopenia

tomaculous neuropathy

tongue, enlarged

transient neurologic deficit

treatment of neurologic disorder

tricresylphosphate

trigeminal nerve

trigeminal nerve, hypertrophy

trigeminal neuralgia

trinucleotide repeats

ulnar neuropathy

ultrasonography, nerve

urinary incontinence

Usher's syndrome

vestibular function, tests of

vibratory sensation, abnormal

vincristine neurotoxicity

viral infection

vision, failure of in childhood

visual acuity, decreased

visual evoked response

visual field defect

visual fields, constricted

visual impairment

visual loss, congenital

vitreous opacities

vocal cord paralysis

voice, abnormality of

weakness, generalized

weakness, progressive

weakness, proximal

Werdnig-Hoffman disease

white matter disease

wide based gait

winging of scapula

X-linked neuropathy

Showing articles 50 to 100 of 5224 << Previous Next >>

DNA Analysis in Finnish Patients with Hereditary Neuropathy with Liability to Pressure Palsies (HNPP)
JNNP 57:1260-1262, Silander,K.,et al, 1994

Liver Transplantation as a Treatment for Familial Amyloidotic Polyneuropathy
Ann Int Med 120:133-134, Skinner,M.,et al, 1994

Clinical Genetics in Neurological Disease
JNNP 57:7-15, MacMillan,J.C.&Harper,P.S., 1994

Erythromelalgia:Association with Hereditary Sensory Neuropathy and Response to Amitriptyline
Neurol 43:621-622, Herskovitz,S.,et al, 1993

Hereditary Motor-Sensory Neuropathy (Charcot-Marie-Tooth Disease) with Nerve Deafness:A New Variant
J Pediatr 123:431-434, Hamiel,O.P.,et al, 1993

Charcot-Marie-Tooth Disease Type 1A:Association with a Spontaneous Point Mutation in the PMP22 Gene
NEJM 329:96-101, Roa,B.B.,et al, 1993

Inherited Primary Peripheral Neuropathies
JAMA 270:2326, 23301993., Lupski,J.R.,et al, 1993

Duplication of Part of Chromosome 17 is Commonly Associated with HMSN Type I (Charcot-Marie-Tooth Disease Type 1)
Ann Neurol 31:570-572, Hallam,P.J.,et al, 1992

De-Novo Mutation in Hereditary Motor and Sensory Neuropathy Type I
Lancet 339:1081-1082, Hoogendijk,J.E.,et al, 1992

Brain MRI and Electrophysiologic Abnormalities in Preclinical and Clinical Adrenomyeloneuropathy
Neurol 42:85-91, Aubourg,P.,et al, 1992

Corticosteroid-Responsive Dominantly Inherited Neuropathy in Childhood
Neurol 41:437-439, Bird,S.J.&Sladky,J.T., 1991

Genetic Linkage of Hereditary Motor & SensoryNeuro Type I (Charcot-Marie-Tooth Disease) to Chrom 1 & 17
Neurol 40:1450-1453, Defesche,J.C.,et al, 1990

Tangier Disease in a Black Patient:An Unusual Clinical Presentation
Am J Med 89:105-108, Lo,W.D.,et al, 1990

Hereditary Motor and Sensory Neuropathies and Hereditary Spastic Paraplegia:A Magnetic Stimulation Study
Ann Neurol 28:43-49, Claus,D.,et al, 1990

Refsum Disease
In Rowland's Merritt's Textbk of Neurology, Lea & Febiger, Phila, 8thEd, p. 509, Menkes,J.H., 1989

Friedreich Ataxia
In Rowland, L. P. Merritt's Textbook of Neurology, 8th Ed, Lea & Febiger, Phila, Ch 13, p627, Rosenberg,R.N., 1989

REcurrent Familial Brachial Plexus Palsies as the ONly Clinical Expression of'Tomaculous'Neuropathy
Eur Neurol 29:61-66, Martinelli,P.,et al, 1989

Molecular Genetics of Amyloid Neuropathy in Europe
Lancet 1:524-526, Holt,I.J.,et al, 1989

Hereditary Sensory Neuropathy with Deafness:A Familial Multisystem Atrophy
Neurol 39:244-248, Horoupian,D.S., 1989

Respiratory Muscle Weakness in Charcot-Marie-Tooth Disease, A Field Study
Arch Int med 149:1389-1391, Nathanson,B.N.,et al, 1989

Hereditary Motor & Sensory Neuropathy with Optic Atrophy, Ultrastructural and Morphometic Observations
Arch Neurol 46:973-977, Sommer,C.&Schroder,J.M., 1989

Compression Syndromes Due to Hypertrophic Nerve Roots in Hereditary Motor Sensory Neuropathy Type I
Neurol 39:1173-1177, Rosen,S.A.,et al, 1989

Follow-up and Diagnostic Reappraisal of 75 Patients with Leber's Congenital Amaurosis
Am J Ophthalmol 107:624-631, Lambert,S.R.,et al, 1989

Familial Oculoleptomeningeal Amyloidosis, Report of a New Family with Unusual Features
Arch Neurol 45:1118-1122, Uitti,R.J.,et al, 1988

Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I
Arch Int Med 148:1739-1740, Eichacker,P.Q.,et al, 1988

Retinitis Pigmentosa
Surv Ophthalmol 33:137-177, Pagon,R.A., 1988

Hereditary Neuropathy with Liability to Pressure Palsies
In Handbk of Clin Neurol, Elsevier Sci Publ Co, NY 51:551-562987., Cherry,S.&Mayer,R.F., 1987

Hereditary Motor & Sensory Neuropathy, X-Linked:A Half Century Follow-Up
Neurol 37:1460-1465, Rozear,M.P.,et al, 1987

Ocular Complications of Tangier Disease
Am J Med 83:991-994, Pressley,T.A.,et al, 1987

Chronic Demyelinating Peripheral Neuropathy in Cerebrotendinous Xanthomatosis
Ann Neurol 20:89-91, Argov,Z.,et al, 1986

Tangier Disease (Hypo-a-Lipoproteinemia)
Textbook of Child Neurology, 3rd Ed. , Phila, Lea & Febiger, Ch 1, p 86, Menkes,J.H., 1985

Neurogenic Arthropathy & Recurring Fractures with Subclinical Inherited Neuropathy
Neurol 33:357-367, Dyck,P.J.,et al, 1983

Clinicopathological Conference
Maroteaux-Lamy Syndrome, Case 44-1983, NEJM 309:1109-1117983., , 1983

Exacerbation of Charcot-Marie-Tooth Disease in Pregnancy
Neurol 32:1311-1314, Pollock,M.,et al, 1982

Intensive Evaluation of Referred Unclassified Neuropathies Yields Improved Diagnosis
Ann Neurol 10:222-226, Dyck,P.J.,et al, 1981

Bilateral Vocal Cord Paralysis in a Patient With Familial Hypertrophic Neuropathy
Arch Neurol 38:532, Johnson,J.A.,et al, 1981

Pattern Reversal Visual Evoked Potentials
Arch Neurol 38:739-741, Bird,T.D.,et al, 1981

Dejerine-Sottas Disease Revisited
Arch Neurol 37:67-68, Stran,R., 1980

Central Vestibular Involvement in Peroneal Muscle Atrophy:A Preliminary Report
Ann Neurol 5:118-120, Melgaard,B.,et al, 1979

Cervical Myelographic Changes in Hypertrophic Interstitial Polyneuropathy
Ann Neurol 2:83, Hammerschlag,S.B.,et al, 1977

Nerve Growth Factor (three parts)
NEJM 297:1096, 1149, 1211977., Mobley,W.C.,et al, 1977

Myasthenic Abduction Nystagmus in a Patient with Hyperthyroidism
Neurol 26:589, Finelli,P.F.&Hoyt,W., 1976

Nerve-Growth Factor in Familial Dysautonomia
NEJM 295:671, Montalcini,R.L., 1976

Charcot-Marie-Tooth Disease Associated With"Essential Tremor"
Neurol Sciences 28:17-40, Salisachs,P.J., 1976

Scalloped Pupils in Familial Amyloidosis
NEJM 293:914, Lessell,S.,et al, 1975

Neurotoxicity of Commonly Used Antineoplastic Agents
NEJM 291:75, 1271974., Weiss,H.,et al, 1974

Epidemiology of Motor-Neuron Diseases
NEJM 288:1047, Bobwick,A.R.,et al, 1973

Polyneroupathies of Undetermined Cause
Acta Neurol Scand (Supp) :5970., Prineas,J., 1970

Lower Motor & Primary Sensory Neuron Diseases with Peroneal Muscular Atrophy
Arch Neurol 18:603, Dyck,P.,et al, 1968

Lower Motor & Primary Sensory Neuron Diseases with Peroneal Muscular Atrophy (II)
Arch Neurol 18:619, Dyck,P.,et al, 1968

Showing articles 50 to 100 of 5224 << Previous Next >>